Alternative Names & Classifications:
Acquired Molybdenum Cofactor Deficiency (CLINICAL)
Description
Molybdenum is a crucial trace element required for the activation of vital enzymes like sulfite oxidase, xanthine oxidase, and aldehyde oxidase. Acquired deficiency is almost exclusively documented in patients sustained on long-term total parenteral nutrition that lacks an integrated trace mineral formulation. Without functional sulfite oxidase, highly toxic sulfites rapidly accumulate in the body, leading to severe neurological deterioration.